Ilayda Korkmaz1, Banu Yaman2, Naim Ceylan3, Mehmet Kantar4, Serra Kamer5, Melis Palamar11Department of Ophthalmology, Ege University Faculty of Medicine, Izmir, Türkiye 2Department of Pathology, Ege University Faculty of Medicine, Izmir, Türkiye 3Department of Radiology, Ege University Faculty of Medicine, Izmir, Türkiye 4Department of Pediatrics, Division of Pediatric Oncology, Ege University Faculty of Medicine, Izmir, Türkiye 5Department of Radiation Oncology, Ege University Faculty of Medicine, Izmir, Türkiye
Orbital rhabdomyosarcoma is the most common malignant orbital tumor of childhood originating from mesenchymal cells. The presenting symptom is usually acute onset unilateral proptosis. The rapidly progressive course of the findings may resemble infectious and inflammatory orbital diseases. Radiological imaging and histopathological examinations are crucial for differential diagnosis. The main goal of treatment with a multidisciplinary approach is to control both local and distant spread of the tumor and to prevent further damage. With the introduction of chemotherapy and radiotherapy in the treatment, the overall survival rate has in-creased. Thus, aggressive surgical approach for complete removal of the tumor has been abandoned.
Keywords: Orbital rhabdomyosarcoma, orbital tumor; proptosis.