ISSN 2757-8135 | E-ISSN 2757-9816
European Eye Research
Orbital rhabdomyosarcoma: Review [Eur Eye Res]
Eur Eye Res. Ahead of Print: EER-02996 | DOI: 10.14744/eer.2022.02996

Orbital rhabdomyosarcoma: Review

Ilayda Korkmaz1, Banu Yaman2, Naim Ceylan3, Mehmet Kantar4, Serra Kamer5, Melis Palamar1
1Department of Ophthalmology, Ege University Faculty of Medicine, Izmir, Türkiye
2Department of Pathology, Ege University Faculty of Medicine, Izmir, Türkiye
3Department of Radiology, Ege University Faculty of Medicine, Izmir, Türkiye
4Department of Pediatrics, Division of Pediatric Oncology, Ege University Faculty of Medicine, Izmir, Türkiye
5Department of Radiation Oncology, Ege University Faculty of Medicine, Izmir, Türkiye

Orbital rhabdomyosarcoma is the most common malignant orbital tumor of childhood originating from mesenchymal cells. The presenting symptom is usually acute onset unilateral proptosis. The rapidly progressive course of the findings may resemble infectious and inflammatory orbital diseases. Radiological imaging and histopathological examinations are crucial for differential diagnosis. The main goal of treatment with a multidisciplinary approach is to control both local and distant spread of the tumor and to prevent further damage. With the introduction of chemotherapy and radiotherapy in the treatment, the overall survival rate has in-creased. Thus, aggressive surgical approach for complete removal of the tumor has been abandoned.

Keywords: Orbital rhabdomyosarcoma, orbital tumor; proptosis.



Corresponding Author: Melis Palamar, Türkiye
Manuscript Language: English